Fifty-seven percent of the cases were associated with polycystic kidneys, and the majority of the cases presented with epigastric fullness, flank pain, or gross hematuria.
Fifty-seven percent of the cases were associated with polycystic kidneys, and the majority of the cases presented with epigastric fullness, flank pain, or gross hematuria.
总胆管肿之平均发病年龄为13.2±19.8岁，以女性占绝大多数(86%)，其中1例女性合并先天性肝纤维化。